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Google Keyword Rankings for : treatment von gierke's disease
1
Dietary Therapy for Von Gierke's Disease: A Case Report - NCBI
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5630462/
Dietary therapy was started as frequent meals with high carbohydrate content, including nocturnal feeds. Later on, uncooked cornstarch, ...
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https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5630462/
Dietary therapy was started as frequent meals with high carbohydrate content, including nocturnal feeds. Later on, uncooked cornstarch, ...
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2
Treatment of Von Gierke Disease - Medindia
https://www.medindia.net/patients/patientinfo/von-gierke-disease-treatment.htm
The primary goal of treatment of Von Gierke Disease is to avoid low blood sugar. Diet is the mainstay of treatment and requires close ...
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https://www.medindia.net/patients/patientinfo/von-gierke-disease-treatment.htm
The primary goal of treatment of Von Gierke Disease is to avoid low blood sugar. Diet is the mainstay of treatment and requires close ...
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3
Type Ia Glycogen Storage Disease Treatment & Management
https://emedicine.medscape.com/article/119318-treatment
In general, no specific treatment exists to cure glycogen storage diseases (GSDs). In most cases, the mainstay of management involves measures ...
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https://emedicine.medscape.com/article/119318-treatment
In general, no specific treatment exists to cure glycogen storage diseases (GSDs). In most cases, the mainstay of management involves measures ...
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4
Glycogen Storage Disease Type I - NORD (National ...
https://rarediseases.org/rare-diseases/glycogen-storage-disease-type-i/
GSDI is treated with a special diet in order to maintain normal glucose levels, prevent hypoglycemia and maximize growth and development. Frequent small ...
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https://rarediseases.org/rare-diseases/glycogen-storage-disease-type-i/
GSDI is treated with a special diet in order to maintain normal glucose levels, prevent hypoglycemia and maximize growth and development. Frequent small ...
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5
Glycogen Storage Disease (GSD) - Cleveland Clinic
https://my.clevelandclinic.org/health/diseases/15553-glycogen-storage-disease-gsd
Treatment consists of taking regular doses of uncooked cornstarch and/or nutrition supplements. Cornstarch is a complex carbohydrate that is ...
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https://my.clevelandclinic.org/health/diseases/15553-glycogen-storage-disease-gsd
Treatment consists of taking regular doses of uncooked cornstarch and/or nutrition supplements. Cornstarch is a complex carbohydrate that is ...
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6
Glucose-6-phosphatase deficiency (glycogen storage disease ...
https://www.uptodate.com/contents/glucose-6-phosphatase-deficiency-glycogen-storage-disease-i-von-gierke-disease
... known as von Gierke disease, is a glycogen storage disease (GSD). ... Treatment is focused on maintenance of physiologic glucose levels.
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https://www.uptodate.com/contents/glucose-6-phosphatase-deficiency-glycogen-storage-disease-i-von-gierke-disease
... known as von Gierke disease, is a glycogen storage disease (GSD). ... Treatment is focused on maintenance of physiologic glucose levels.
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7
Gene therapy for glycogen storage diseases - Oxford Academic
https://academic.oup.com/hmg/article/28/R1/R31/5520922
There is no effective treatment for this disease, but many patients are able to perform moderate, sustained exercise on a carbohydrate-rich diet with ...
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https://academic.oup.com/hmg/article/28/R1/R31/5520922
There is no effective treatment for this disease, but many patients are able to perform moderate, sustained exercise on a carbohydrate-rich diet with ...
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8
Von Gierke disease | Multimedia Encyclopedia
https://www.stlukes-stl.com/health-content/health-ency-multimedia/1/000338.htm
The goal of treatment is to avoid low blood sugar. Eat frequently during the day, especially foods that contain carbohydrates (starches). Older ...
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https://www.stlukes-stl.com/health-content/health-ency-multimedia/1/000338.htm
The goal of treatment is to avoid low blood sugar. Eat frequently during the day, especially foods that contain carbohydrates (starches). Older ...
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9
Von Gierke Disease Symptoms, Doctors, Treatments ...
https://www.medifind.com/conditions/von-gierke-disease/5457
The goal of treatment is to avoid low blood sugar. Eat frequently during the day, especially foods that contain carbohydrates (starches). Older children and ...
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https://www.medifind.com/conditions/von-gierke-disease/5457
The goal of treatment is to avoid low blood sugar. Eat frequently during the day, especially foods that contain carbohydrates (starches). Older children and ...
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10
Glycogen Storage Disease - Boston Children's Hospital
https://www.childrenshospital.org/conditions/glycogen-storage-disease
Glycogen storage disease type I (GSD I), also known as von Gierke disease, accounts for about 25 percent of all children with GSD. Symptoms typically appear ...
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https://www.childrenshospital.org/conditions/glycogen-storage-disease
Glycogen storage disease type I (GSD I), also known as von Gierke disease, accounts for about 25 percent of all children with GSD. Symptoms typically appear ...
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11
Glycogen Storage Disease | Johns Hopkins Medicine
https://www.hopkinsmedicine.org/health/conditions-and-diseases/glycogen-storage-disease
› health › glycogen-s...
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https://www.hopkinsmedicine.org/health/conditions-and-diseases/glycogen-storage-disease
› health › glycogen-s...
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12
Pediatric Glycogen Storage Disease | Children's Pittsburgh
https://www.chp.edu/our-services/transplant/liver/education/liver-disease-states/glycogen-storage-diseases
Type I - Von Gierke Disease · Enlarged liver and kidneys · Low blood sugar · High levels of lactate, fats, and uric acid in the blood · Impaired growth and delayed ...
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https://www.chp.edu/our-services/transplant/liver/education/liver-disease-states/glycogen-storage-diseases
Type I - Von Gierke Disease · Enlarged liver and kidneys · Low blood sugar · High levels of lactate, fats, and uric acid in the blood · Impaired growth and delayed ...
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13
Glycogen Storage Disease Type 1 (von Gierke)
https://liverfoundation.org/liver-diseases/pediatric-liver-disease/glycogen-storage-disease-1-and-2/
How is GSD I treated? The treatment of type I glycogen storage disease is focused on correcting the metabolic changes in the body and promoting ...
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https://liverfoundation.org/liver-diseases/pediatric-liver-disease/glycogen-storage-disease-1-and-2/
How is GSD I treated? The treatment of type I glycogen storage disease is focused on correcting the metabolic changes in the body and promoting ...
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14
Diagnosis and management of glycogen storage disease type I
https://www.nature.com/articles/gim2014128
Consensus was developed in each area of diagnosis, treatment, ... In 1929, von Gierke described glycogen storage disease type I (GSD I) ...
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https://www.nature.com/articles/gim2014128
Consensus was developed in each area of diagnosis, treatment, ... In 1929, von Gierke described glycogen storage disease type I (GSD I) ...
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15
Von Gierke's Glycogen Storage Disease - Patient.info
https://patient.info/doctor/von-gierkes-glycogen-storage-disease
The main aim of treatment is to correct hypoglycaemia and maintain normoglycaemia: · Intake of fructose and galactose should be restricted, as ...
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https://patient.info/doctor/von-gierkes-glycogen-storage-disease
The main aim of treatment is to correct hypoglycaemia and maintain normoglycaemia: · Intake of fructose and galactose should be restricted, as ...
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16
A Simple Guide To Von Gierke Disease, (Glycogen Storage ...
https://www.amazon.com/Glycogen-Disorder-Diagnosis-Treatment-Conditions-ebook/dp/B07HRWS2C5
› Glycogen-Disorder-Diagnos...
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https://www.amazon.com/Glycogen-Disorder-Diagnosis-Treatment-Conditions-ebook/dp/B07HRWS2C5
› Glycogen-Disorder-Diagnos...
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17
Glycogen Storage Disease Type I - ScienceDirect.com
https://www.sciencedirect.com/topics/medicine-and-dentistry/glycogen-storage-disease-type-i
Treatment is symptomatic and aims to prevent hypoglycemia while ensuring adequate nutrition. A high-carbohydrate, high-protein diet and frequent feeding are ...
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https://www.sciencedirect.com/topics/medicine-and-dentistry/glycogen-storage-disease-type-i
Treatment is symptomatic and aims to prevent hypoglycemia while ensuring adequate nutrition. A high-carbohydrate, high-protein diet and frequent feeding are ...
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18
von Gierke disease causes, symptoms, diagnosis, treatment ...
https://healthjade.net/von-gierke-disease/
von Gierke disease is treated with a special diet in order to maintain normal glucose levels, prevent hypoglycemia and maximize growth and development. Frequent ...
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https://healthjade.net/von-gierke-disease/
von Gierke disease is treated with a special diet in order to maintain normal glucose levels, prevent hypoglycemia and maximize growth and development. Frequent ...
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19
Dietary Therapy for Von Gierke's Disease: A Case Report
https://www.semanticscholar.org/paper/Dietary-Therapy-for-Von-Gierke%E2%80%99s-Disease%3A-A-Case-Raza-Arif/e5621a64ea4d815e86a49c0f19669459e3e93a14
Von Gierke's disease, also known as glycogen storage disease (GSD) type 1A, ... confirmed with a liver biopsy and dietary treatment was started.
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https://www.semanticscholar.org/paper/Dietary-Therapy-for-Von-Gierke%E2%80%99s-Disease%3A-A-Case-Raza-Arif/e5621a64ea4d815e86a49c0f19669459e3e93a14
Von Gierke's disease, also known as glycogen storage disease (GSD) type 1A, ... confirmed with a liver biopsy and dietary treatment was started.
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20
von Gierke disease - Health Library
http://nch.adam.com/content.aspx?productid=117&pid=1&gid=000338
The goal of treatment is to avoid low blood sugar. Eat frequently during the day, especially foods that contain carbohydrates (starches). Older ...
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http://nch.adam.com/content.aspx?productid=117&pid=1&gid=000338
The goal of treatment is to avoid low blood sugar. Eat frequently during the day, especially foods that contain carbohydrates (starches). Older ...
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21
Von Gierke Disease, (Glycogen Storage ... - Barnes & Noble
https://www.barnesandnoble.com/w/von-gierke-disease-kenneth-kee/1129689285
Oct 4, 2018 —
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https://www.barnesandnoble.com/w/von-gierke-disease-kenneth-kee/1129689285
Oct 4, 2018 —
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22
Glycogen storage disease type I (patient information) - wikidoc
https://www.wikidoc.org/index.php/Glycogen_storage_disease_type_I_(patient_information)
Since treatments have been developed, growth, puberty, and quality of life have improved for people with von Gierke disease.
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https://www.wikidoc.org/index.php/Glycogen_storage_disease_type_I_(patient_information)
Since treatments have been developed, growth, puberty, and quality of life have improved for people with von Gierke disease.
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23
(PDF) Dietary Therapy for Von Gierke's Disease: A Case Report
https://www.researchgate.net/publication/318993752_Dietary_Therapy_for_Von_Gierke's_Disease_A_Case_Report
Von Gierke's disease, also known as glycogen storage disease (GSD) type 1A, is an autosomal recessive disease in which there is an inability ...
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https://www.researchgate.net/publication/318993752_Dietary_Therapy_for_Von_Gierke's_Disease_A_Case_Report
Von Gierke's disease, also known as glycogen storage disease (GSD) type 1A, is an autosomal recessive disease in which there is an inability ...
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24
World's first gene therapy for glycogen storage disease ...
https://www.sciencedaily.com/releases/2019/09/190920124645.htm
The gene therapy works by delivering a new copy of a gene to the liver via a naturally occurring virus. Administered through the patient's ...
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https://www.sciencedaily.com/releases/2019/09/190920124645.htm
The gene therapy works by delivering a new copy of a gene to the liver via a naturally occurring virus. Administered through the patient's ...
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25
Glycogen storage disease type Ib - Myriad Genetics
https://myriad.com/womens-health/diseases/glycogen-storage-disease-type-ib/
The treatment of GSDIb involves careful monitoring of the affected individual's diet, both in the frequency of meals and type of foods eaten. Individuals with ...
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https://myriad.com/womens-health/diseases/glycogen-storage-disease-type-ib/
The treatment of GSDIb involves careful monitoring of the affected individual's diet, both in the frequency of meals and type of foods eaten. Individuals with ...
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26
Glycogen Storage Disease Type 1 / Von Gierke ... - YouTube
https://www.youtube.com/watch?v=e_foq3bcNZM
Dr.G Bhanu Prakash Animated Medical Videos
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https://www.youtube.com/watch?v=e_foq3bcNZM
Dr.G Bhanu Prakash Animated Medical Videos
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27
Research yields potential treatment approach for glycogen ...
https://corporate.dukehealth.org/news/research-yields-potential-treatment-approach-glycogen-storage-disease
... glycogen storage disease Ia, known as GSDIa or von Gierke disease, a genetic metabolic disorder that requires lifelong dietary therapy.
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https://corporate.dukehealth.org/news/research-yields-potential-treatment-approach-glycogen-storage-disease
... glycogen storage disease Ia, known as GSDIa or von Gierke disease, a genetic metabolic disorder that requires lifelong dietary therapy.
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28
Glycogen storage diseases: Diagnosis, treatment and outcome
https://content.iospress.com/articles/translational-science-of-rare-diseases/trd006
The aim of treatment is to prevent hypoglycemia and counter-regulation thereby minimizing the secondary metabolic derangements. Therapy may ...
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https://content.iospress.com/articles/translational-science-of-rare-diseases/trd006
The aim of treatment is to prevent hypoglycemia and counter-regulation thereby minimizing the secondary metabolic derangements. Therapy may ...
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29
Glycogen storage disease type I - Wikipedia
https://en.wikipedia.org/wiki/Glycogen_storage_disease_type_I
› wiki › Glycogen_storage_dis...
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https://en.wikipedia.org/wiki/Glycogen_storage_disease_type_I
› wiki › Glycogen_storage_dis...
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30
VON GIERKE DISEASE: NEW TRENDS IN MANAGEMENT
http://www.scielo.org.co/scielo.php?script=sci_abstract&pid=S0121-52562012000200007&lng=e&nrm=iso&tlng=en
No cure has been found for this disease and it can turn out to be lethal if no appropriate management is given during the first two decades of life. The ...
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http://www.scielo.org.co/scielo.php?script=sci_abstract&pid=S0121-52562012000200007&lng=e&nrm=iso&tlng=en
No cure has been found for this disease and it can turn out to be lethal if no appropriate management is given during the first two decades of life. The ...
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31
Glycogen Storage Diseases - Cancer Care of Western New York
https://www.cancercarewny.com/content.aspx?chunkiid=22629
Type 0, Liver glycogen synthase deficiency; Type 1, Von Gierke disease, defect in glucose-6-phosphatase enzyme, the most common type of GSD accounting for ...
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https://www.cancercarewny.com/content.aspx?chunkiid=22629
Type 0, Liver glycogen synthase deficiency; Type 1, Von Gierke disease, defect in glucose-6-phosphatase enzyme, the most common type of GSD accounting for ...
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32
von gierke disease: Topics by Science.gov
https://www.science.gov/topicpages/v/von+gierke+disease
Gene therapy research has generated proof-of-concept for GSD types I (von Gierke disease) and II (Pompe disease). Key features of these gene therapy ...
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https://www.science.gov/topicpages/v/von+gierke+disease
Gene therapy research has generated proof-of-concept for GSD types I (von Gierke disease) and II (Pompe disease). Key features of these gene therapy ...
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33
Glycogen storage disease type I | Radiology Reference Article
https://radiopaedia.org/articles/glycogen-storage-disease-type-i?lang=us
Glycogen storage disease type I (GSD-I), also known as von Gierke disease, is a type of glycogen storage disease where there is excess ...
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https://radiopaedia.org/articles/glycogen-storage-disease-type-i?lang=us
Glycogen storage disease type I (GSD-I), also known as von Gierke disease, is a type of glycogen storage disease where there is excess ...
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34
Research, therapies and new treatments
https://ninalaguerrera.org/en/research-and-therapies/
Nina, the Von Gierke's warrior! Menu. III International Charity Hike Nina the Warrior (VIRTUAL); Glycogen Storage Disease (GSD). What is GSD? Control ...
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https://ninalaguerrera.org/en/research-and-therapies/
Nina, the Von Gierke's warrior! Menu. III International Charity Hike Nina the Warrior (VIRTUAL); Glycogen Storage Disease (GSD). What is GSD? Control ...
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35
Glycogen Storage Disease Type I Article - StatPearls
https://www.statpearls.com/ArticleLibrary/viewarticle/31267
Glycogen storage disease type I (GSD I), also known as Von Gierke disease, ... Dietary treatment prevents hypoglycemia and improves the life ...
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https://www.statpearls.com/ArticleLibrary/viewarticle/31267
Glycogen storage disease type I (GSD I), also known as Von Gierke disease, ... Dietary treatment prevents hypoglycemia and improves the life ...
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36
von Gierke's disease | pathology - Encyclopedia Britannica
https://www.britannica.com/science/von-Gierkes-disease
Certain symptoms vary according to the specific disorder, but, in general, affected individuals have a poor appetite or unusual food preferences (e.g., aversion ...
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https://www.britannica.com/science/von-Gierkes-disease
Certain symptoms vary according to the specific disorder, but, in general, affected individuals have a poor appetite or unusual food preferences (e.g., aversion ...
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37
Von Gierke Disease (GSD1) - AGSD-UK
https://agsd.org.uk/all-about-gsd/gsd-variants/von-gierke-disease-gsd1/gsd1-section4-tab1/
On 24 July 2018 a patient received the first ever gene therapy for glycogen storage disease (GSD). It was developed by the team led by Dr. David Weinstein, ...
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https://agsd.org.uk/all-about-gsd/gsd-variants/von-gierke-disease-gsd1/gsd1-section4-tab1/
On 24 July 2018 a patient received the first ever gene therapy for glycogen storage disease (GSD). It was developed by the team led by Dr. David Weinstein, ...
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38
Von Gierke Disease, (Glycogen Storage Disorder I) A ... - Scribd
https://www.scribd.com/book/390137482/Von-Gierke-Disease-Glycogen-Storage-Disorder-I-A-Simple-Guide-To-The-Condition-Diagnosis-Treatment-And-Related-Conditions
› Ebooks › Medical
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https://www.scribd.com/book/390137482/Von-Gierke-Disease-Glycogen-Storage-Disorder-I-A-Simple-Guide-To-The-Condition-Diagnosis-Treatment-And-Related-Conditions
› Ebooks › Medical
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39
Continuous glucose monitoring in the treatment of obesity in ...
https://edm.bioscientifica.com/view/journals/edm/2014/1/EDM13-0056.xml
Glycogen storage disease (GSD) type Ia (von Gierke's disease) is an inherited (autosomal recessive transmission) metabolic disorder of glycogen metabolism, ...
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https://edm.bioscientifica.com/view/journals/edm/2014/1/EDM13-0056.xml
Glycogen storage disease (GSD) type Ia (von Gierke's disease) is an inherited (autosomal recessive transmission) metabolic disorder of glycogen metabolism, ...
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40
Von Gierke Disease - Picmonic
https://www.picmonic.com/api/v3/picmonics/2542/pdf
Von Gierke's disease is a type I glycogen storage disease cause by a deficiency in glucose-6-phosphatase. This key enzyme is used for breaking down glycogen ...
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https://www.picmonic.com/api/v3/picmonics/2542/pdf
Von Gierke's disease is a type I glycogen storage disease cause by a deficiency in glucose-6-phosphatase. This key enzyme is used for breaking down glycogen ...
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41
Youngmok Lee, Ph.D | Department of Pediatrics - UConn Health
https://health.uconn.edu/dept-pediatrics/gsd/
Importantly, shedding light on GSDs will benefit treatment not only for the patients with GSDs but also for the general ... GSD-I, Von Gierke's Disease.
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https://health.uconn.edu/dept-pediatrics/gsd/
Importantly, shedding light on GSDs will benefit treatment not only for the patients with GSDs but also for the general ... GSD-I, Von Gierke's Disease.
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42
Glycogen Storage Disease (GSD)
https://www.chop.edu/conditions-diseases/glycogen-storage-disease-gsd
Treatment of glycogen storage disease. Currently, there is no cure for GSD. Treatment will vary depending on what type of GSD your child has; however, the ...
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https://www.chop.edu/conditions-diseases/glycogen-storage-disease-gsd
Treatment of glycogen storage disease. Currently, there is no cure for GSD. Treatment will vary depending on what type of GSD your child has; however, the ...
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43
Daily Management - CureGSD
https://www.curegsd.org/gsd-daily-management
Glycogen Storage Disease was almost always fatal until 1971, when it was discovered that continuous glucose therapy could prevent hypoglycemia. In 1982 ...
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https://www.curegsd.org/gsd-daily-management
Glycogen Storage Disease was almost always fatal until 1971, when it was discovered that continuous glucose therapy could prevent hypoglycemia. In 1982 ...
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44
Glycogen Storage Disease in Children | Cedars-Sinai
https://www.cedars-sinai.org/health-library/diseases-and-conditions---pediatrics/g/glycogen-storage-disease-in-children.html
Each GSD has its own symptoms and needs different treatment. The most common types of GSD are types I, III, and IV: Type I or von Gierke's disease.
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https://www.cedars-sinai.org/health-library/diseases-and-conditions---pediatrics/g/glycogen-storage-disease-in-children.html
Each GSD has its own symptoms and needs different treatment. The most common types of GSD are types I, III, and IV: Type I or von Gierke's disease.
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45
Impact of glycogen storage disease type I on adult daily life
https://ojrd.biomedcentral.com/articles/10.1186/s13023-021-02006-w
by SF Garbade · 2021 · Cited by 5 —
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https://ojrd.biomedcentral.com/articles/10.1186/s13023-021-02006-w
by SF Garbade · 2021 · Cited by 5 —
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46
Glycogen Storage Disease Description - Pediatric Home Service
https://www.pediatrichomeservice.com/patient-conditions/glycogen-storage-diseases/
Meet Joe'Von ... PHS Home Care for Patients With Glycogen Storage Diseases ... Type O – Lewis' disease – Liver; Type Ia & b – von Gierke's disease – Liver, ...
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https://www.pediatrichomeservice.com/patient-conditions/glycogen-storage-diseases/
Meet Joe'Von ... PHS Home Care for Patients With Glycogen Storage Diseases ... Type O – Lewis' disease – Liver; Type Ia & b – von Gierke's disease – Liver, ...
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47
A Study of mRNA-3745 in Participants With Glycogen Storage ...
https://clinicaltrials.gov/ct2/show/NCT05095727
Condition or disease, Intervention/treatment, Phase. Glycogen Storage Disease, Drug: mRNA-3745, Phase 1 ... Von Gierke disease
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https://clinicaltrials.gov/ct2/show/NCT05095727
Condition or disease, Intervention/treatment, Phase. Glycogen Storage Disease, Drug: mRNA-3745, Phase 1 ... Von Gierke disease
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48
A Case of von Gierke Disease
https://www.e-cep.org/m/makeCookie.php?url=/m/journal/view.php?number=1997401217
Cornstarch dietary therapy for him had favorable responses showing improvement of hypoglycemia, other metabolic derangements, and regression of hepatomegaly.
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https://www.e-cep.org/m/makeCookie.php?url=/m/journal/view.php?number=1997401217
Cornstarch dietary therapy for him had favorable responses showing improvement of hypoglycemia, other metabolic derangements, and regression of hepatomegaly.
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49
Von Gierke disease - Orphanet
https://www.orpha.net/consor/cgi-bin/Disease_Search.php?lng=EN&data_id=645&Disease_Disease_Search_diseaseType=ORPHA&Disease_Disease_Search_diseaseGroup=364&Disease(s)/group%20of%20diseases=Von-Gierke-disease&title=Von-Gierke-disease&search=Disease_Search_Simple
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50
Search Orphan Drug Designations and Approvals - FDA
https://www.accessdata.fda.gov/scripts/opdlisting/oopd/detailedIndex.cfm?cfgridkey=536016
Treatment of glycogen storage disease type Ia (von Gierke Disease) · Designated · Not FDA Approved for Orphan Indication · Ultragenyx Pharmaceutical, Inc. 60 ...
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https://www.accessdata.fda.gov/scripts/opdlisting/oopd/detailedIndex.cfm?cfgridkey=536016
Treatment of glycogen storage disease type Ia (von Gierke Disease) · Designated · Not FDA Approved for Orphan Indication · Ultragenyx Pharmaceutical, Inc. 60 ...
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51
Glycogen Storage Diseases - Winchester Hospital
https://www.winchesterhospital.org/health-library/article?id=22629
The goal of treatment for these types is to prevent the blood glucose levels from getting too low. This is done by having cornstarch and eating a lot of protein ...
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https://www.winchesterhospital.org/health-library/article?id=22629
The goal of treatment for these types is to prevent the blood glucose levels from getting too low. This is done by having cornstarch and eating a lot of protein ...
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52
Von Gierke's Glycogen Disease
https://www.ccjm.org/content/ccjom/13/1/34.full.pdf
A better understanding of its pathogenesis and treatment will probably come through study of enzymatic activity within the liver. S U M M A R Y. In the two ...
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https://www.ccjm.org/content/ccjom/13/1/34.full.pdf
A better understanding of its pathogenesis and treatment will probably come through study of enzymatic activity within the liver. S U M M A R Y. In the two ...
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53
Adeno‐associated virus gene therapy prevents hepatocellular ...
https://aasldpubs.onlinelibrary.wiley.com/doi/full/10.1002/hep.25894
In contrast to most other inborn errors of metabolism, enzyme‐replacement therapy is not possible for von Gierke's disease because the ...
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https://aasldpubs.onlinelibrary.wiley.com/doi/full/10.1002/hep.25894
In contrast to most other inborn errors of metabolism, enzyme‐replacement therapy is not possible for von Gierke's disease because the ...
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54
Research: Glycogen storage disease type I
https://rarediseases.oscar.ncsu.edu/disease/glycogen-storage-disease-type-i/research/
... form of glycogen storage disease, hepatorenal glycogenosis, von Gierke disease, ... It may take many years to treat enough patients to determine if a ...
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https://rarediseases.oscar.ncsu.edu/disease/glycogen-storage-disease-type-i/research/
... form of glycogen storage disease, hepatorenal glycogenosis, von Gierke disease, ... It may take many years to treat enough patients to determine if a ...
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55
VON GIERKE'S DISEASE or GLYCOGEN STORAGE ...
https://flipper.diff.org/app/items/6219
Treatment should achieve normal glucose, lactic acid, and electrolyte levels, and only mild elevations of uric acid and triglycerides. Avoidance ...
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https://flipper.diff.org/app/items/6219
Treatment should achieve normal glucose, lactic acid, and electrolyte levels, and only mild elevations of uric acid and triglycerides. Avoidance ...
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56
Liver Glycogen Disease (Von Gierke's Disease) - JAMA Network
https://jamanetwork.com/journals/jamainternalmedicine/fullarticle/567301
Liver glycogen disease (von Gierke's disease) is a rare and incompletely understood disorder of childhood, characterized by high concentration of glycogen ...
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https://jamanetwork.com/journals/jamainternalmedicine/fullarticle/567301
Liver glycogen disease (von Gierke's disease) is a rare and incompletely understood disorder of childhood, characterized by high concentration of glycogen ...
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57
Glycogen Storage Disorders - Pediatrics - Medbullets Step 2/3
https://step2.medbullets.com/pediatrics/120122/glycogen-storage-disorders
genetic testing. identification of pathogenic variants in the PYGM gene. gives definitive diagnosis. Treatment. Von Gierke disease (type 1).
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https://step2.medbullets.com/pediatrics/120122/glycogen-storage-disorders
genetic testing. identification of pathogenic variants in the PYGM gene. gives definitive diagnosis. Treatment. Von Gierke disease (type 1).
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58
Glycogen Storage Disease Type IA, Von Gierke ... - Embark
https://embarkvet.com/products/dog-health/health-conditions/glycogen-storage-disease-type-ia-von-gierke-disease-gsd-ia/
How is this condition treated? There is no treatment except supportive care for the clinical signs the affected dog develops. What actions should I take if my ...
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https://embarkvet.com/products/dog-health/health-conditions/glycogen-storage-disease-type-ia-von-gierke-disease-gsd-ia/
How is this condition treated? There is no treatment except supportive care for the clinical signs the affected dog develops. What actions should I take if my ...
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59
Von Gierke Disease, (Glycogen Storage Disorder ... - Goodreads
https://www.goodreads.com/book/show/42184763-von-gierke-disease-glycogen-storage-disorder-i-a-simple-guide-to-the
Read reviews from the world's largest community for readers. This book describes Von Gierke Disease, Diagnosis and Treatment and Related ...
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https://www.goodreads.com/book/show/42184763-von-gierke-disease-glycogen-storage-disorder-i-a-simple-guide-to-the
Read reviews from the world's largest community for readers. This book describes Von Gierke Disease, Diagnosis and Treatment and Related ...
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60
von Gierke's disease | World Problems & Global Issues
http://encyclopedia.uia.org/en/problem/174181
Without proper treatment, GSD I gives rise to chronic low blood sugar, which can result in derangements including excessive levels of lactic ...
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http://encyclopedia.uia.org/en/problem/174181
Without proper treatment, GSD I gives rise to chronic low blood sugar, which can result in derangements including excessive levels of lactic ...
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61
Gastric cancer following a liver transplantation for glycogen ...
https://www.spandidos-publications.com/10.3892/ol.2014.2599
Glycogen storage disease type Ia (GSD‑Ia; also termed von Gierke disease) is an inherited metabolic disorder resulting from a ...
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https://www.spandidos-publications.com/10.3892/ol.2014.2599
Glycogen storage disease type Ia (GSD‑Ia; also termed von Gierke disease) is an inherited metabolic disorder resulting from a ...
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62
Von Gierke's Disease - SlideShare
https://www.slideshare.net/franndjamen/von-gierkes-disease
GENERAL INTRODUCTION • HISTORY • CAUSES OF DISEASE • SIGNS AND SYMPTOMS • LABORATORY DIAGNOSIS • TREATMENT • END. 3. Glycogen storage disorders are classified ...
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https://www.slideshare.net/franndjamen/von-gierkes-disease
GENERAL INTRODUCTION • HISTORY • CAUSES OF DISEASE • SIGNS AND SYMPTOMS • LABORATORY DIAGNOSIS • TREATMENT • END. 3. Glycogen storage disorders are classified ...
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63
Glycogen storage disease type I - bionity.com
https://www.bionity.com/en/encyclopedia/Glycogen_storage_disease_type_I.html
Long-term management should eliminate hypoglycemic symptoms and maintain normal growth. Treatment should achieve normal glucose, lactic acid, and electrolyte ...
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https://www.bionity.com/en/encyclopedia/Glycogen_storage_disease_type_I.html
Long-term management should eliminate hypoglycemic symptoms and maintain normal growth. Treatment should achieve normal glucose, lactic acid, and electrolyte ...
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64
Glycogen Storage Disease Type 1a - JScreen
https://jscreen.org/learn-more/diseases/glycogen-storage-disease-type-1a
The treatment of GSD type Ia involves a careful monitoring of the affected person's diet, both in frequency of meals and type of foods eaten. People with GSD ...
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https://jscreen.org/learn-more/diseases/glycogen-storage-disease-type-1a
The treatment of GSD type Ia involves a careful monitoring of the affected person's diet, both in frequency of meals and type of foods eaten. People with GSD ...
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65
p0235 / #981: extracorporeal membrane oxygenation as a ...
https://journals.lww.com/pccmjournal/Fulltext/2021/03001/P0235____981__EXTRACORPOREAL_MEMBRANE_OXYGENATION.294.aspx
Aims & Objectives: Glycogen storage disease (GSD) type Ia (Von Gierke's Disease) ... of Extracorporeal Membrane Oxygenation (ECMO) to treat this condition.
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https://journals.lww.com/pccmjournal/Fulltext/2021/03001/P0235____981__EXTRACORPOREAL_MEMBRANE_OXYGENATION.294.aspx
Aims & Objectives: Glycogen storage disease (GSD) type Ia (Von Gierke's Disease) ... of Extracorporeal Membrane Oxygenation (ECMO) to treat this condition.
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66
Liver transplantation for type I and type IV glycogen storage ...
https://link.springer.com/article/10.1007/BF02072093
One patient had glycogen storage disease (GSD) type I (von Gierke disease) and seven patients had type IV GSD (Andersen disease).
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https://link.springer.com/article/10.1007/BF02072093
One patient had glycogen storage disease (GSD) type I (von Gierke disease) and seven patients had type IV GSD (Andersen disease).
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67
Glycogen Storage Disease in Dogs - PetMD
https://www.petmd.com/dog/conditions/endocrine/c_multi_glycogen_storage_disease
Upon diagnosis, your dog will need to be continuously monitored and treated for hypoglycemia. However, there is not much that can be done to ...
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https://www.petmd.com/dog/conditions/endocrine/c_multi_glycogen_storage_disease
Upon diagnosis, your dog will need to be continuously monitored and treated for hypoglycemia. However, there is not much that can be done to ...
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68
Glycogen Storage Disease Type I (GSD I) - Verywell Health
https://www.verywellhealth.com/glycogen-storage-disease-type-1-symptoms-causes-and-treatment-6499554
There is no proven treatment or cure for GSD I. However, the disease can be managed with dietary therapy. This requires following special diet ...
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https://www.verywellhealth.com/glycogen-storage-disease-type-1-symptoms-causes-and-treatment-6499554
There is no proven treatment or cure for GSD I. However, the disease can be managed with dietary therapy. This requires following special diet ...
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69
Glycogen Storage Disease in Children
https://www.spectrumhealthlakeland.org/lakeland-diabetes/diabetes-health-library/Content/134/227/
Each GSD has its own symptoms and needs different treatment. The most common types of GSD are types I, III, and IV: Type I or von Gierke disease.
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https://www.spectrumhealthlakeland.org/lakeland-diabetes/diabetes-health-library/Content/134/227/
Each GSD has its own symptoms and needs different treatment. The most common types of GSD are types I, III, and IV: Type I or von Gierke disease.
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70
Anaplerotic Therapy Using Triheptanoin for Patients With ...
https://www.centerwatch.com/clinical-trials/listings/212287/anaplerotic-therapy-using-triheptanoin-for-patients-with-glycogen-storage-disease-type-i/
Clinical trial for Von Gierke's disease , Anaplerotic Therapy Using Triheptanoin for Patients With Glycogen Storage Disease Type I.
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https://www.centerwatch.com/clinical-trials/listings/212287/anaplerotic-therapy-using-triheptanoin-for-patients-with-glycogen-storage-disease-type-i/
Clinical trial for Von Gierke's disease , Anaplerotic Therapy Using Triheptanoin for Patients With Glycogen Storage Disease Type I.
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71
Glycogen storage disease type Ia and Ib
https://womenshealth.labcorp.com/sites/default/files/2021-10/Glycogen%20storage%20disease%20type%20Ia%20and%20Ib_0317_0_0.pdf
What is glycogen storage disease type I? Glycogen storage disease type I, also called von Gierke disease,1 is an inherited disease caused by a defect in the.
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https://womenshealth.labcorp.com/sites/default/files/2021-10/Glycogen%20storage%20disease%20type%20Ia%20and%20Ib_0317_0_0.pdf
What is glycogen storage disease type I? Glycogen storage disease type I, also called von Gierke disease,1 is an inherited disease caused by a defect in the.
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72
von Gierke disease | Montreal Gazette
https://montrealgazette.com/other/von-gierke-disease
The goal of treatment is to avoid low blood sugar. Eat frequently during the day, especially foods that contain carbohydrates (starches). Older ...
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https://montrealgazette.com/other/von-gierke-disease
The goal of treatment is to avoid low blood sugar. Eat frequently during the day, especially foods that contain carbohydrates (starches). Older ...
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73
Glycogen storage diseases: hematological aspects
https://www.cancertherapyadvisor.com/home/decision-support-in-medicine/hematology/glycogen-storage-diseases-hematological-aspects/
Glucose-6-phosphatase deficiency (GSD type I, von Gierke's disease) is an AR disease ... However, for GSD II (Pompe disease), enzyme replacement therapy is ...
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https://www.cancertherapyadvisor.com/home/decision-support-in-medicine/hematology/glycogen-storage-diseases-hematological-aspects/
Glucose-6-phosphatase deficiency (GSD type I, von Gierke's disease) is an AR disease ... However, for GSD II (Pompe disease), enzyme replacement therapy is ...
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74
Glycogen storage disorders: Pathology review - Osmosis
https://www.osmosis.org/learn/Glycogen_storage_disorders:_Pathology_review
Treatment of von Gierke disease is aimed at controlling its metabolic dysfunction. For hypoglycemia, individuals require a diet rich in complex ...
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https://www.osmosis.org/learn/Glycogen_storage_disorders:_Pathology_review
Treatment of von Gierke disease is aimed at controlling its metabolic dysfunction. For hypoglycemia, individuals require a diet rich in complex ...
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75
effects of cornstarch therapy and other implications of ... - AAPD
https://www.aapd.org/globalassets/media/publications/archives/farrington-17-04.pdf
The essential quality of blood glucose support provided by glycogen degradation is nowhere better illustrated than in glycogenosis, type I (von Gierke's disease) ...
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https://www.aapd.org/globalassets/media/publications/archives/farrington-17-04.pdf
The essential quality of blood glucose support provided by glycogen degradation is nowhere better illustrated than in glycogenosis, type I (von Gierke's disease) ...
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76
An Adult Case of Type Ib Glycogen-Storage Disease
https://www.nejm.org/doi/full/10.1056/NEJM198303103081004
Type I glycogen-storage disease (von Gierke's disease) is due to a deficiency of glucose-6-phosphatase.1 In a variant form of this disease, ...
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https://www.nejm.org/doi/full/10.1056/NEJM198303103081004
Type I glycogen-storage disease (von Gierke's disease) is due to a deficiency of glucose-6-phosphatase.1 In a variant form of this disease, ...
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77
Von Gierke disease (type Ia glycogen storage ... - AK Lectures
https://aklectures.com/lecture/glycogen-storage-diseases/von-gierke-disease-type-ia-glycogen-storage-disease
This lecture will cover the pathophysiology, clinical presentation, treatment and diagnosis of Von Gierke disease. + SHOW MORE. This lecture doesn't have any ...
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https://aklectures.com/lecture/glycogen-storage-diseases/von-gierke-disease-type-ia-glycogen-storage-disease
This lecture will cover the pathophysiology, clinical presentation, treatment and diagnosis of Von Gierke disease. + SHOW MORE. This lecture doesn't have any ...
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78
The Glycogen Storage Disorders | Pediatrics In Review
https://publications.aap.org/pediatricsinreview/article/41/1/41/35328/The-Glycogen-Storage-Disorders
Enzyme replacement therapy with alglucosidas-alpha; high protein diet. ... Occurring in approximately 1 in 50,000 births, von Gierke disease ...
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https://publications.aap.org/pediatricsinreview/article/41/1/41/35328/The-Glycogen-Storage-Disorders
Enzyme replacement therapy with alglucosidas-alpha; high protein diet. ... Occurring in approximately 1 in 50,000 births, von Gierke disease ...
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79
Brasil - Glicogenose Tipo I (Doença de Von Gierke) - SciELO
https://www.scielo.br/j/abc/a/zkRDt54fxfHxsZTLnYJJYbB/?lang=en
Glycogen Storage Disease Type I (Von Gierke disease): Report of Two Cases with Severe ... Despite regular adherence to treatment, total cholesterol and, ...
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https://www.scielo.br/j/abc/a/zkRDt54fxfHxsZTLnYJJYbB/?lang=en
Glycogen Storage Disease Type I (Von Gierke disease): Report of Two Cases with Severe ... Despite regular adherence to treatment, total cholesterol and, ...
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80
Pediatric Glycogen Storage Disease - Children's Health
https://www.childrens.com/specialties-services/conditions/glycogen-storage-disease
Also called Von Gierke disease, this is the most common type of glycogen storage disease. In type I, the enzyme in the liver that is needed to turn glycogen ...
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https://www.childrens.com/specialties-services/conditions/glycogen-storage-disease
Also called Von Gierke disease, this is the most common type of glycogen storage disease. In type I, the enzyme in the liver that is needed to turn glycogen ...
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81
The Medical Bookman
https://www.tandfonline.com/doi/pdf/10.1080/00325481.1959.11712586
fibrinogenemia, Von Gierke's disease, sorne forms ... nosis and treatment of each disease. ... sary for the detection and study of these diseases.
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https://www.tandfonline.com/doi/pdf/10.1080/00325481.1959.11712586
fibrinogenemia, Von Gierke's disease, sorne forms ... nosis and treatment of each disease. ... sary for the detection and study of these diseases.
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82
Glycogen Storage Disease, Type 1a (GSD1A)
https://www.childrenscolorado.org/conditions-and-advice/conditions-and-symptoms/conditions/glycogen-storage-disease/
... storage disease. See how our specialists diagnose and treat GSD1a. ... Glycogen storage disease, Type 1a, is also called GSD1a or Von Gierke disease.
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https://www.childrenscolorado.org/conditions-and-advice/conditions-and-symptoms/conditions/glycogen-storage-disease/
... storage disease. See how our specialists diagnose and treat GSD1a. ... Glycogen storage disease, Type 1a, is also called GSD1a or Von Gierke disease.
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83
Dietary Management of the Glycogen Storage Diseases
https://europepmc.org/article/med/31665208
This article chronicles the evolution of dietary management and treatment of the hepatic GSDs ... Type Ia (von Gierke disease), G6PC (glucose-6-phosphatase) ...
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https://europepmc.org/article/med/31665208
This article chronicles the evolution of dietary management and treatment of the hepatic GSDs ... Type Ia (von Gierke disease), G6PC (glucose-6-phosphatase) ...
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84
von Gierke disease - Symptoms, Causes and Cure - TabletWise
https://www.tabletwise.net/health/von-gierke-disease
Alternative Medicine for Treatment of von Gierke disease · Iron supplements: Helps to maintain iron level · Vitamin D supplements: Helps to ...
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https://www.tabletwise.net/health/von-gierke-disease
Alternative Medicine for Treatment of von Gierke disease · Iron supplements: Helps to maintain iron level · Vitamin D supplements: Helps to ...
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85
Portacaval shunt in the treatment of glycogen storage disease
https://www.surgjournal.com/article/0039-6060(69)90119-6/fulltext
An 18-month-old girl with severe glycogen storage disease, type I (von Gierke's disease), was seen for recurrent episodes of severe hypoglycemia, ...
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https://www.surgjournal.com/article/0039-6060(69)90119-6/fulltext
An 18-month-old girl with severe glycogen storage disease, type I (von Gierke's disease), was seen for recurrent episodes of severe hypoglycemia, ...
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86
Frequently Asked Questions about GSDs
https://www.agsdus.org/faq.php
A: Children with glycogen storage diseases associated with low blood sugar ... (one who has been on treatment and the other with no special treatment) could ...
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https://www.agsdus.org/faq.php
A: Children with glycogen storage diseases associated with low blood sugar ... (one who has been on treatment and the other with no special treatment) could ...
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87
ANAESTHESIA FOR PORTOCAVAL BYPASS IN PATIENTS ...
https://www.bjanaesthesia.org.uk/article/S0007-0912(17)47607-0/pdf
The biochemical lesions of the glycogen storage diseases and of familial ... Observations recorded in seven patients treated for Von Gierke's disease.
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https://www.bjanaesthesia.org.uk/article/S0007-0912(17)47607-0/pdf
The biochemical lesions of the glycogen storage diseases and of familial ... Observations recorded in seven patients treated for Von Gierke's disease.
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88
Glycogen Storage Disease Type Ia: Current Management ...
https://www.mdpi.com/2072-6643/13/11/3828/htm
The unmet need for treatment strategies that address the cause of disease, ... disease type Ia (GSDIa; OMIM#232200), also known as von Gierke disease, ...
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https://www.mdpi.com/2072-6643/13/11/3828/htm
The unmet need for treatment strategies that address the cause of disease, ... disease type Ia (GSDIa; OMIM#232200), also known as von Gierke disease, ...
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89
Glycogen storage disease type I (GSD I)
https://atlasgeneticsoncology.org/cancer-prone-disease/10071/glycogen-storage-disease-type-i-(gsd-i)
Diet is the basis of the treatment (Rake et al., 2002). It aims at avoiding hypoglycemia, combining, in infants, frequent meals and quite often ...
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https://atlasgeneticsoncology.org/cancer-prone-disease/10071/glycogen-storage-disease-type-i-(gsd-i)
Diet is the basis of the treatment (Rake et al., 2002). It aims at avoiding hypoglycemia, combining, in infants, frequent meals and quite often ...
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90
Citations to Studies in Glycogen Storage Diseases. I ... - JCI
https://www.jci.org/articles/view/105230/citations
› articles › view › citations
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https://www.jci.org/articles/view/105230/citations
› articles › view › citations
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91
understanding glycogen storage disease
https://adultmetabolicdiseasesclinic.ca/resources/Infosheets/GSD-1a-essentials.pdf
What is Glycogen storage disease type 1a (von Gierke disease)? ... People with GSD type 1a, even if treated, are often not as tall as family members,.
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https://adultmetabolicdiseasesclinic.ca/resources/Infosheets/GSD-1a-essentials.pdf
What is Glycogen storage disease type 1a (von Gierke disease)? ... People with GSD type 1a, even if treated, are often not as tall as family members,.
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92
Glycogen storage disease type 5 - CheckOrphan
https://checkorphan.org/disease/glycogen-storage-disease-type-5/
Uncooked cornstarch is given and acts as a slow-release form of glucose. Treatment includes a low-fat diet with normal amounts of protein and ...
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https://checkorphan.org/disease/glycogen-storage-disease-type-5/
Uncooked cornstarch is given and acts as a slow-release form of glucose. Treatment includes a low-fat diet with normal amounts of protein and ...
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93
Von Gierke Disease - Abertay University
https://rke.abertay.ac.uk/en/publications/von-gierke-disease
The disease is currently managed by nocturnal nasogastric infusion of glucose and/or cornstarch mixed into drinks during the day, but compliance ...
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https://rke.abertay.ac.uk/en/publications/von-gierke-disease
The disease is currently managed by nocturnal nasogastric infusion of glucose and/or cornstarch mixed into drinks during the day, but compliance ...
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94
Three consecutive pregnancies in a patient with glycogen ...
https://www.ajog.org/article/S0002-9378(94)70342-6/abstract
Glycogen storage disease type IA, or von Gierke's disease, is an autosomal ... Treatment is aimed at maintenance of near-normal blood glucose concentrations ...
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https://www.ajog.org/article/S0002-9378(94)70342-6/abstract
Glycogen storage disease type IA, or von Gierke's disease, is an autosomal ... Treatment is aimed at maintenance of near-normal blood glucose concentrations ...
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95
Glycogen Storage Diseases and Disorders of Gluconeogenesis
https://www.merckmanuals.com/en-ca/professional/multimedia/table/glycogen-storage-diseases-and-disorders-of-gluconeogenesis
GSD I (von Gierke disease) ... Treatment: Uncooked cornstarch 1.5–2.5 g/kg orally every 4–6 hours or lactose-free ... GSD II (Pompe disease; 232300*).
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https://www.merckmanuals.com/en-ca/professional/multimedia/table/glycogen-storage-diseases-and-disorders-of-gluconeogenesis
GSD I (von Gierke disease) ... Treatment: Uncooked cornstarch 1.5–2.5 g/kg orally every 4–6 hours or lactose-free ... GSD II (Pompe disease; 232300*).
→ Check Latest Keyword Rankings ←
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